Cancer UrologyCancer UrologyОнкоурология1726-97761996-1812Publishing House ABV Press77810.17650/1726-9776-2017-13-4-126-132CLINICAL CASEКЛИНИЧЕСКИЙ СЛУЧАЙMetastatic renal cell carcinoma kidney in children 10 years old – possibility of targeted therapyМетастатический почечно-клеточный рак почки у ребенка 10 лет. Возможности таргетной терапии (клиническое наблюдение)PavlovA. Yu.ПавловА. Ю.
Russian Federation

86 Profsoyuznaya St., Moscow 117997

17997 Москва, ул. Профсоюзная, 86

SabirzyanovaZ. R.СабирзяноваЗ. Р.
Russian Federation

86 Profsoyuznaya St., Moscow 117997

Зухра Рустамовна Сабирзянова..

17997 Москва, ул. Профсоюзная, 86

sabirzianova@yandex.ruZheludkovaO. G.ЖелудковаО. Г.
Russian Federation

86 Profsoyuznaya St., Moscow 117997

17997 Москва, ул. Профсоюзная, 86

MikhalchenkoA. V.МихальченкоА. В.
Russian Federation

86 Profsoyuznaya St., Moscow 117997

17997 Москва, ул. Профсоюзная, 86

Russian Scientific Center of Roentgen RadiologyФГБУ «Российский научный центр рентгенорадиологии» Минздрава России301220171341261321701201817012018https://oncourology.abvpress.ru/oncur/article/view/778

Renal cell carcinoma (RCC) is rare in children, its metastatic form is even rarer. At present there is no treatment protocol for children with RCC. This clinical observation presented the patient 10 year old with RCC metastases to the lungs. After radical surgery, after targeted sorafenib therapy the patient has a positive dynamics. At present his progression-free survival is 30 months.

Почечно-клеточный рак (ПКР) редко встречается у детей, а его метастатическая форма еще реже. На настоящий момент не существует протоколов лечения для детей с ПКР, не изучены возможности современной таргетной терапии. В данной статье представлено клиническое наблюдение пациента 10 лет с ПКР и метастазами в легкие. После тотального удаления опухоли почки на фоне проведения таргетной терапии сорафенибом у пациента достигнута положительная динамика. В настоящий момент выживаемость без прогрессирования составляет 30 мес.

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